                         SEQUENCE LISTING

<110>  University of Utah Research Foundation
 
<120>  Compositions and Methods for Treating Peroxisomal Biogenesis 
       Disorders

<130>  21101.0400P1

<150>  US 62/873,119
<151>  2019-07-11

<160>  2     

<170>  PatentIn version 3.5

<210>  1
<211>  361
<212>  PRT
<213>  Homo sapiens

<400>  1

Met Val His Ala Glu Ala Phe Ser Arg Pro Leu Ser Arg Asn Glu Val 
1               5                   10                  15      


Val Gly Leu Ile Phe Arg Leu Thr Ile Phe Gly Ala Val Thr Tyr Phe 
            20                  25                  30          


Thr Ile Lys Trp Met Val Asp Ala Ile Asp Pro Thr Arg Lys Gln Lys 
        35                  40                  45              


Val Glu Ala Gln Lys Gln Ala Glu Lys Leu Met Lys Gln Ile Gly Val 
    50                  55                  60                  


Lys Asn Val Lys Leu Ser Glu Tyr Glu Met Ser Ile Ala Ala His Leu 
65                  70                  75                  80  


Val Asp Pro Leu Asn Met His Val Thr Trp Ser Asp Ile Ala Gly Leu 
                85                  90                  95      


Asp Asp Val Ile Thr Asp Leu Lys Asp Thr Val Ile Leu Pro Ile Lys 
            100                 105                 110         


Lys Lys His Leu Phe Glu Asn Ser Arg Leu Leu Gln Pro Pro Lys Gly 
        115                 120                 125             


Val Leu Leu Tyr Gly Pro Pro Gly Cys Gly Lys Thr Leu Ile Ala Lys 
    130                 135                 140                 


Ala Thr Ala Lys Glu Ala Gly Cys Arg Phe Ile Asn Leu Gln Pro Ser 
145                 150                 155                 160 


Thr Leu Thr Asp Lys Trp Tyr Gly Glu Ser Gln Lys Leu Ala Ala Ala 
                165                 170                 175     


Val Phe Ser Leu Ala Ile Lys Leu Gln Pro Ser Ile Ile Phe Ile Asp 
            180                 185                 190         


Glu Ile Asp Ser Phe Leu Arg Asn Arg Ser Ser Ser Asp His Glu Ala 
        195                 200                 205             


Thr Ala Met Met Lys Ala Gln Phe Met Ser Leu Trp Asp Gly Leu Asp 
    210                 215                 220                 


Thr Asp His Ser Cys Gln Val Ile Val Met Gly Ala Thr Asn Arg Pro 
225                 230                 235                 240 


Gln Asp Leu Asp Ser Ala Ile Met Arg Arg Met Pro Thr Arg Phe His 
                245                 250                 255     


Ile Asn Gln Pro Ala Leu Lys Gln Arg Glu Ala Ile Leu Lys Leu Ile 
            260                 265                 270         


Leu Lys Asn Glu Asn Val Asp Arg His Val Asp Leu Leu Glu Val Ala 
        275                 280                 285             


Gln Glu Thr Asp Gly Phe Ser Gly Ser Asp Leu Lys Glu Met Cys Arg 
    290                 295                 300                 


Asp Ala Ala Leu Leu Cys Val Arg Glu Tyr Val Asn Ser Thr Ser Glu 
305                 310                 315                 320 


Glu Ser His Asp Glu Asp Glu Ile Arg Pro Val Gln Gln Gln Asp Leu 
                325                 330                 335     


His Arg Ala Ile Glu Lys Met Lys Lys Ser Lys Asp Ala Ala Phe Gln 
            340                 345                 350         


Asn Val Leu Thr His Val Cys Leu Asp 
        355                 360     


<210>  2
<211>  361
<212>  PRT
<213>  Mus musculus

<400>  2

Met Val His Ala Glu Ala Phe Ser Arg Pro Leu Ser Arg Asn Glu Val 
1               5                   10                  15      


Val Gly Leu Ile Phe Arg Leu Thr Ile Phe Gly Ala Val Thr Tyr Phe 
            20                  25                  30          


Thr Ile Lys Trp Met Val Asp Ala Ile Asp Pro Thr Arg Lys Gln Lys 
        35                  40                  45              


Val Glu Ala Gln Lys Gln Ala Glu Lys Leu Met Lys Gln Ile Gly Val 
    50                  55                  60                  


Lys Asn Val Lys Leu Ser Glu Tyr Glu Met Ser Ile Ala Ala His Leu 
65                  70                  75                  80  


Val Asp Pro Leu Asn Met His Val Thr Trp Ser Asp Ile Ala Gly Leu 
                85                  90                  95      


Asp Asp Val Ile Thr Asp Leu Lys Asp Thr Val Ile Leu Pro Ile Lys 
            100                 105                 110         


Lys Lys His Leu Phe Glu Asn Ser Arg Leu Leu Gln Pro Pro Lys Gly 
        115                 120                 125             


Val Leu Leu Tyr Gly Pro Pro Gly Cys Gly Lys Thr Leu Ile Ala Lys 
    130                 135                 140                 


Ala Thr Ala Lys Glu Ala Gly Cys Arg Phe Ile Asn Leu Gln Pro Ser 
145                 150                 155                 160 


Thr Leu Thr Asp Lys Trp Tyr Gly Glu Ser Gln Lys Leu Ala Ala Ala 
                165                 170                 175     


Val Phe Ser Leu Ala Ile Lys Leu Gln Pro Ser Ile Ile Phe Ile Asp 
            180                 185                 190         


Glu Ile Asp Ser Phe Leu Arg Asn Arg Ser Ser Ser Asp His Glu Ala 
        195                 200                 205             


Thr Ala Met Met Lys Ala Gln Phe Met Ser Leu Trp Asp Gly Leu Asp 
    210                 215                 220                 


Thr Asp His Ser Cys Gln Val Ile Val Met Gly Ala Thr Asn Arg Pro 
225                 230                 235                 240 


Gln Asp Leu Asp Ser Ala Ile Met Arg Arg Met Pro Thr Arg Phe His 
                245                 250                 255     


Ile Asn Gln Pro Ala Leu Lys Gln Arg Glu Ala Ile Leu Lys Leu Ile 
            260                 265                 270         


Leu Lys Asn Glu Asn Val Asp Arg His Val Asp Leu Leu Glu Val Ala 
        275                 280                 285             


Gln Glu Thr Asp Gly Phe Ser Gly Ser Asp Leu Lys Glu Met Cys Arg 
    290                 295                 300                 


Asp Ala Ala Leu Leu Cys Val Arg Glu Tyr Val Asn Ser Thr Ser Glu 
305                 310                 315                 320 


Glu Ser His Asp Glu Asp Glu Ile Arg Pro Val Gln Gln Gln Asp Leu 
                325                 330                 335     


His Arg Ala Ile Glu Lys Met Lys Lys Ser Lys Asp Ala Ala Phe Gln 
            340                 345                 350         


Asn Val Leu Thr His Val Cys Leu Asp 
        355                 360     


