﻿               SEQUENCE LISTING

<110> UNIVERSITE GRENOBLE ALPES 
	  INSERM
      UNIVERSITE DE PARIS XI PARIS SUD 
      CENTRE HOSPITALIER UNIVERSITAIRE GRENOBLE ALPES 

<120> INHIBITEUR D’ACYL-THIOESTERASES POUR LE TRAITEMENT ET/OU LA PREVENTION DE LA MALADIE DE HUNTINGTON

<130> B25305FR

<160> 2

<170> BiSSAP 1.3.6

<210> 1
<211> 408
<212> DNA
<213> Homo sapiens


<220> 
<223> exon 1 de la Huntingtine

<400> 1
gctgccggga cgggtccaag atggacggcc gctcaggttc tgcttttacc tgcggcccag      60

agccccattc attgccccgg tgctgagcgg cgccgcgagt cggcccgagg cctccgggga     120

ctgccgtgcc gggcgggaga ccgccatggc gaccctggaa aagctgatga aggccttcga     180

gtccctcaag tccttccagc agcagcagca gcagcagcag cagcagcagc agcagcagca     240

gcagcagcag cagcaacagc cgccaccgcc gccgccgccg ccgccgcctc ctcagcttcc     300

tcagccgccg ccgcaggcac agccgctgct gcctcagccg cagccgcccc cgccgccgcc     360

cccgccgcca cccggcccgg ctgtggctga ggagccgctg caccgacc                  408


<210> 2
<211> 6038
<212> DNA
<213> Séquence artificielle 


<220> 
<223> Plasmide RUSH Str-KDEL_SBP-mCherry-GPI

<400> 2
gacggatcgg gagatctccc gatcccctat ggtcgactct cagtacaatc tgctctgatg       60

ccgcatagtt aagccagtat ctgctccctg cttgtgtgtt ggaggtcgct gagtagtgcg      120

cgagcaaaat ttaagctaca acaaggcaag gcttgaccga caattgcatg aagaatctgc      180

ttagggttag gcgttttgcg ctgcttcgcg atgtacgggc cagatatacg cgttgacatt      240

gattattgac tagttattaa tagtaatcaa ttacggggtc attagttcat agcccatata      300

tggagttccg cgttacataa cttacggtaa atggcccgcc tggctgaccg cccaacgacc      360

cccgcccatt gacgtcaata atgacgtatg ttcccatagt aacgccaata gggactttcc      420

attgacgtca atgggtggac tatttacggt aaactgccca cttggcagta catcaagtgt      480

atcatatgcc aagtacgccc cctattgacg tcaatgacgg taaatggccc gcctggcatt      540

atgcccagta catgacctta tgggactttc ctacttggca gtacatctac gtattagtca      600

tcgctattac catggtgatg cggttttggc agtacatcaa tgggcgtgga tagcggtttg      660

actcacgggg atttccaagt ctccacccca ttgacgtcaa tgggagtttg ttttggcacc      720

aaaatcaacg ggactttcca aaatgtcgta acaactccgc cccattgacg caaatgggcg      780

gtaggcgtgt acggtgggag gtctatataa gcagagctct ctggctaact agagaaccca      840

ctgcttactg gcttatcgaa attaatacga ctcactatag ggagacccaa gcttggtacc      900

gagctcggat cgatatctgc ggcctagcta gcgcttaagg cctgttaacc ggtatggatg      960

tatgcgtccg tcttgccctg tggctcctct ggggactcct cctgcaccag ggccagagcc     1020

tcagccatag tcacagtgag aaggcgacag gaaccagctc gggcgccggt ttaaacgacc     1080

ctagcaaaga ctcaaaagct caggtgtccg ctgccgaggc tggcattact ggaacatggt     1140

acaatcagct cgggagcacc tttattgtga ctgctggagc cgatggagcc ctcaccggaa     1200

catacgaatc tgctgtggga aacgccgaat cacggtacgt cctcactggc cgatacgata     1260

gtgcccctgc caccgacgga tctgggactg ccctgggatg gactgtcgct tggaaaaaca     1320

actaccggaa tgctcattct gccacaacat ggagtggaca gtacgtggga ggcgctgagg     1380

ctagaatcaa tacacagtgg ctgctcacat ctggcacaac cgaggcaaat gcttggaaat     1440

ccaccctggt gggacatgac acattcacca aagtgaaacc ctccgccgct tcaatcgatg     1500

ccgccaaaaa agccggagtc aacaacggca atcctctgga tgccgtccag cagctcggac     1560

cgaaagatga actgtgagcg gccgcataga taactgatcc agtgtgctgg aattaattcg     1620

ctgtctgcga gggccagctg ttggggtgag tactccctct caaaagcggg catgacttct     1680

gcgctaagat tgtcagtttc caaaaacgag gaggatttga tattcacctg gcccgcggtg     1740

atgcctttga gggtggccgc gtccatctgg tcagaaaaga caatcttttt gttgtcaagc     1800

ttgaggtgtg gcaggcttga gatctggcca tacacttgag tgacaatgac atccactttg     1860

cctttctctc cacaggtgtc cactcccagg tccaactgca ggtcgagcat gcatctaggg     1920

cggccaattc cgcccctctc cctccccccc ccctaacgtt actggccgaa gccgcttgga     1980

ataaggccgg tgtgcgtttg tctatatgtt attttccacc atattgccgt cttttggcaa     2040

tgtgagggcc cggaaacctg gccctgtctt cttgacgagc attcctaggg gtctttcccc     2100

tctcgccaaa ggaatgcaag gtctgttgaa tgtcgtgaag gaagcagttc ctctggaagc     2160

ttcttgaaga caaacaacgt ctgtagcgac cctttgcagg cagcggaacc ccccacctgg     2220

cgacaggtgc ctctgcggcc aaaagccacg tgtataagat acacctgcaa aggcggcaca     2280

accccagtgc cacgttgtga gttggatagt tgtggaaaga gtcaaatggc tctcctcaag     2340

cgtattcaac aaggggctga aggatgccca gaaggtaccc cattgtatgg gatctgatct     2400

ggggcctcgg tgcacatgct ttacatgtgt ttagtcgagg ttaaaaaaac gtctaggccc     2460

cccgaaccac ggggacgtgg ttttcctttg aaaaacacga tgataagctt gccacaaccc     2520

gggaggcgcg ccatgtacag gatgcaactc ctgtcttgca ttgcactaag tcttgcactt     2580

gtcacgaatt ccgacgagaa gaccactggt tggcgaggtg gacacgttgt tgaaggactg     2640

gctggggaac ttgaacaact tcgtgcacga ctggagcatc acccacaagg tcaacgtgaa     2700

ccacctgcag gtgtgagcaa gggcgaggag gataacatgg ccatcatcaa ggagttcatg     2760

cgcttcaagg tgcacatgga gggctccgtg aacggccacg agttcgagat cgagggcgag     2820

ggcgagggcc gcccctacga gggcacccag accgccaagc tgaaggtgac caagggtggc     2880

cccctgccct tcgcctggga catcctgtcc cctcagttca tgtacggctc caaggcctac     2940

gtgaagcacc ccgccgacat ccccgactac ttgaagctgt ccttccccga gggcttcaag     3000

tgggagcgcg tgatgaactt cgaggacggc ggcgtggtga ccgtgaccca ggactcctcc     3060

ctacaggacg gcgagttcat ctacaaggtg aagctgcgcg gcaccaactt cccctccgac     3120

ggccccgtaa tgcagaagaa gaccatgggc tgggaggcct cctccgagcg gatgtacccc     3180

gaggacggcg ccctgaaggg cgagatcaag cagaggctga agctgaagga cggcggccac     3240

tacgacgctg aggtcaagac cacctacaag gccaagaagc ccgtgcagct gcccggcgcc     3300

tacaacgtca acatcaagtt ggacatcacc tcccacaacg aggactacac catcgtggaa     3360

cagtacgaac gcgccgaggg ccgccactcc accggcggca tggacgagct gtacaagggc     3420

cggccactgg aaaatggcgg aacctctctg tctgaaaaaa ctgtgctgct gctggtgact     3480

ccctttctgg ccgctgcttg gtccctccac ccatgaggcc tcgagggcca attaattaac     3540

tctagataac tgatcataat cagccatacc acatttgtag aggttttact tgctttaaaa     3600

aacctcccac acctccccct gaacctgaaa cataaaatga atgcaattgt tgttgttaac     3660

ttgtttattg cagcttataa tggttacaaa taaagcaata gcatcacaaa tttcacaaat     3720

aaagcatttt tttcactgca ttctagttgt ggtttgtcca aactcatcaa tgtatcttaa     3780

cgcgtcgagt gcattctagt tgtggtttgt ccaaactcat caatgtatct tatcatgtct     3840

gtataccgtc gacctctagc tagagcttgg cgtaatcatg gtcatagctg tttcctgtgt     3900

gaaattgtta tccgctcaca attccacaca acatacgagc cggaagcata aagtgtaaag     3960

cctggggtgc ctaatgagtg agctaactca cattaattgc gttgcgctca ctgcccgctt     4020

tccagtcggg aaacctgtcg tgccagctgc attaatgaat cggccaacgc gcggggagag     4080

gcggtttgcg tattgggcgc tcttccgctt cctcgctcac tgactcgctg cgctcggtcg     4140

ttcggctgcg gcgagcggta tcagctcact caaaggcggt aatacggtta tccacagaat     4200

caggggataa cgcaggaaag aacatgtgag caaaaggcca gcaaaaggcc aggaaccgta     4260

aaaaggccgc gttgctggcg tttttccata ggctccgccc ccctgacgag catcacaaaa     4320

atcgacgctc aagtcagagg tggcgaaacc cgacaggact ataaagatac caggcgtttc     4380

cccctggaag ctccctcgtg cgctctcctg ttccgaccct gccgcttacc ggatacctgt     4440

ccgcctttct cccttcggga agcgtggcgc tttctcaatg ctcacgctgt aggtatctca     4500

gttcggtgta ggtcgttcgc tccaagctgg gctgtgtgca cgaacccccc gttcagcccg     4560

accgctgcgc cttatccggt aactatcgtc ttgagtccaa cccggtaaga cacgacttat     4620

cgccactggc agcagccact ggtaacagga ttagcagagc gaggtatgta ggcggtgcta     4680

cagagttctt gaagtggtgg cctaactacg gctacactag aaggacagta tttggtatct     4740

gcgctctgct gaagccagtt accttcggaa aaagagttgg tagctcttga tccggcaaac     4800

aaaccaccgc tggtagcggt ggtttttttg tttgcaagca gcagattacg cgcagaaaaa     4860

aaggatctca agaagatcct ttgatctttt ctacggggtc tgacgctcag tggaacgaaa     4920

actcacgtta agggattttg gtcatgagat tatcaaaaag gatcttcacc tagatccttt     4980

taaattaaaa atgaagtttt aaatcaatct aaagtatata tgagtaaact tggtctgaca     5040

gttaccaatg cttaatcagt gaggcaccta tctcagcgat ctgtctattt cgttcatcca     5100

tagttgcctg actccccgtc gtgtagataa ctacgatacg ggagggctta ccatctggcc     5160

ccagtgctgc aatgataccg cgagacccac gctcaccggc tccagattta tcagcaataa     5220

accagccagc cggaagggcc gagcgcagaa gtggtcctgc aactttatcc gcctccatcc     5280

agtctattaa ttgttgccgg gaagctagag taagtagttc gccagttaat agtttgcgca     5340

acgttgttgc cattgctaca ggcatcgtgg tgtcacgctc gtcgtttggt atggcttcat     5400

tcagctccgg ttcccaacga tcaaggcgag ttacatgatc ccccatgttg tgcaaaaaag     5460

cggttagctc cttcggtcct ccgatcgttg tcagaagtaa gttggccgca gtgttatcac     5520

tcatggttat ggcagcactg cataattctc ttactgtcat gccatccgta agatgctttt     5580

ctgtgactgg tgagtactca accaagtcat tctgagaata gtgtatgcgg cgaccgagtt     5640

gctcttgccc ggcgtcaata cgggataata ccgcgccaca tagcagaact ttaaaagtgc     5700

tcatcattgg aaaacgttct tcggggcgaa aactctcaag gatcttaccg ctgttgagat     5760

ccagttcgat gtaacccact cgtgcaccca actgatcttc agcatctttt actttcacca     5820

gcgtttctgg gtgagcaaaa acaggaaggc aaaatgccgc aaaaaaggga ataagggcga     5880

cacggaaatg ttgaatactc atactcttcc tttttcaata ttattgaagc atttatcagg     5940

gttattgtct catgagcgga tacatatttg aatgtattta gaaaaataaa caaatagggg     6000

ttccgcgcac atttccccga aaagtgccac ctgacgtc                             6038


