                         SEQUENCE LISTING

<110>  Case Western Reserve University
 
<120>  TDP-43 MITOCHONDRIAL LOCALIZATION INHIBITOR FOR THE TREATMENT OF 
       NEURODEGENERATIVE DISEASE

<130>  CWR-025431WO ORD

<150>  62/328,484
<151>  2016-04-27

<150>  62/139,580
<151>  2016-04-07

<160>  19    

<170>  PatentIn version 3.5

<210>  1
<211>  7
<212>  PRT
<213>  Homo sapiens

<400>  1

Phe Pro Gly Ala Cys Gly Leu 
1               5           


<210>  2
<211>  8
<212>  PRT
<213>  Homo sapiens

<400>  2

Leu Ile Val Leu Gly Leu Pro Trp 
1               5               


<210>  3
<211>  5
<212>  PRT
<213>  Homo sapiens

<400>  3

Gly Phe Gly Phe Val 
1               5   


<210>  4
<211>  8
<212>  PRT
<213>  Homo sapiens

<400>  4

Ala Phe Ala Phe Val Thr Phe Ala 
1               5               


<210>  5
<211>  7
<212>  PRT
<213>  Homo sapiens

<400>  5

Gly Gly Gly Ala Gly Leu Gly 
1               5           


<210>  6
<211>  7
<212>  PRT
<213>  Homo sapiens

<400>  6

Gly Ala Ala Ile Gly Trp Gly 
1               5           


<210>  7
<211>  9
<212>  PRT
<213>  Homo sapiens

<400>  7

Ala Gln Phe Pro Gly Ala Cys Gly Leu 
1               5                   


<210>  8
<211>  9
<212>  PRT
<213>  Homo sapiens

<400>  8

Ser Lys Gly Phe Gly Phe Val Arg Phe 
1               5                   


<210>  9
<211>  9
<212>  PRT
<213>  Homo sapiens

<400>  9

Ser Arg Gly Gly Gly Ala Gly Leu Gly 
1               5                   


<210>  10
<211>  414
<212>  PRT
<213>  Homo sapiens

<400>  10

Met Ser Glu Tyr Ile Arg Val Thr Glu Asp Glu Asn Asp Glu Pro Ile 
1               5                   10                  15      


Glu Ile Pro Ser Glu Asp Asp Gly Thr Val Leu Leu Ser Thr Val Thr 
            20                  25                  30          


Ala Gln Phe Pro Gly Ala Cys Gly Leu Arg Tyr Arg Asn Pro Val Ser 
        35                  40                  45              


Gln Cys Met Arg Gly Val Arg Leu Val Glu Gly Ile Leu His Ala Pro 
    50                  55                  60                  


Asp Ala Gly Trp Gly Asn Leu Val Tyr Val Val Asn Tyr Pro Lys Asp 
65                  70                  75                  80  


Asn Lys Arg Lys Met Asp Glu Thr Asp Ala Ser Ser Ala Val Lys Val 
                85                  90                  95      


Lys Lys Ala Val Gln Lys Thr Ser Asp Leu Ile Val Leu Gly Leu Pro 
            100                 105                 110         


Trp Lys Thr Thr Glu Gln Asp Leu Lys Glu Tyr Phe Ser Thr Phe Gly 
        115                 120                 125             


Glu Val Leu Met Val Gln Val Lys Lys Asp Leu Lys Thr Gly His Ser 
    130                 135                 140                 


Lys Gly Phe Gly Phe Val Arg Phe Thr Glu Tyr Glu Thr Gln Val Lys 
145                 150                 155                 160 


Val Met Ser Gln Arg His Met Ile Asp Gly Arg Trp Cys Asp Cys Lys 
                165                 170                 175     


Leu Pro Asn Ser Lys Gln Ser Gln Asp Glu Pro Leu Arg Ser Arg Lys 
            180                 185                 190         


Val Phe Val Gly Asx Cys Thr Glu Asp Met Thr Glu Asp Glu Leu Arg 
        195                 200                 205             


Glu Phe Phe Ser Gln Tyr Gly Asp Val Met Asp Val Phe Ile Pro Lys 
    210                 215                 220                 


Pro Phe Arg Ala Phe Ala Phe Val Thr Phe Ala Asp Asp Gln Ile Ala 
225                 230                 235                 240 


Gln Ser Leu Cys Gly Glu Asp Glu Ile Ile Lys Gly Ile Ser Val His 
                245                 250                 255     


Ile Ser Asn Ala Glu Pro Lys His Asn Ser Asn Arg Gln Leu Glu Arg 
            260                 265                 270         


Ser Gly Arg Phe Gly Gly Asn Pro Gly Gly Phe Cys Asn Gln Gly Gly 
        275                 280                 285             


Phe Gly Asn Ser Arg Gly Gly Gly Ala Gly Leu Gly Asn Asn Gln Gly 
    290                 295                 300                 


Ser Asn Met Gly Gly Gly Met Asn Phe Gly Ala Phe Ser Ile Asn Pro 
305                 310                 315                 320 


Ala Met Met Ala Ala Ala Gln Ala Ala Leu Gln Ser Ser Trp Gly Met 
                325                 330                 335     


Met Gly Met Leu Ala Ser Gln Gln Asn Gln Ser Gly Pro Ser Gly Asn 
            340                 345                 350         


Asn Gln Asn Gln Gly Asn Met Gln Arg Glu Pro Asn Gln Ala Phe Gly 
        355                 360                 365             


Ser Gly Asn Asn Ser Tyr Ser Gly Ser Asn Ser Gly Ala Ala Ile Gly 
    370                 375                 380                 


Trp Gly Ser Ala Ser Asn Ala Gly Ser Gly Ser Gly Phe Asn Gly Gly 
385                 390                 395                 400 


Phe Gly Ser Ser Met Asp Ser Lys Ser Ser Gly Trp Gly Met 
                405                 410                 


<210>  11
<211>  11
<212>  PRT
<213>  Homo sapiens

<400>  11

Tyr Gly Arg Lys Lys Arg Arg Gln Arg Arg Arg 
1               5                   10      


<210>  12
<211>  20
<212>  PRT
<213>  Homo sapiens

<400>  12

Tyr Gly Arg Lys Lys Arg Arg Gln Arg Arg Arg Ser Lys Gly Phe Gly 
1               5                   10                  15      


Phe Val Arg Phe 
            20  


<210>  13
<211>  16
<212>  PRT
<213>  Homo sapiens

<400>  13

Tyr Gly Arg Lys Lys Arg Arg Gln Arg Arg Arg Gly Phe Gly Phe Val 
1               5                   10                  15      


<210>  14
<211>  18
<212>  PRT
<213>  Homo sapiens

<400>  14

Tyr Gly Arg Lys Lys Arg Arg Gln Arg Arg Arg Gly Gly Gly Ala Gly 
1               5                   10                  15      


Leu Gly 
        


<210>  15
<211>  20
<212>  PRT
<213>  Homo sapiens

<400>  15

Tyr Gly Arg Lys Lys Arg Arg Gln Arg Arg Arg Ala Gln Phe Pro Gly 
1               5                   10                  15      


Ala Cys Gly Leu 
            20  


<210>  16
<211>  20
<212>  PRT
<213>  Homo sapiens

<400>  16

Tyr Gly Arg Lys Lys Arg Arg Gln Arg Arg Arg Ser Lys Gly Phe Gly 
1               5                   10                  15      


Phe Val Arg Phe 
            20  


<210>  17
<211>  20
<212>  PRT
<213>  Homo sapiens

<400>  17

Tyr Gly Arg Lys Lys Arg Arg Gln Arg Arg Arg Ser Arg Gly Gly Gly 
1               5                   10                  15      


Ala Gly Leu Gly 
            20  


<210>  18
<211>  20
<212>  PRT
<213>  Homo sapiens

<400>  18

Tyr Gly Arg Lys Lys Arg Arg Gln Arg Arg Arg Ala Ala Gln Gly Phe 
1               5                   10                  15      


Gly Cys Pro Leu 
            20  


<210>  19
<211>  19
<212>  PRT
<213>  Homo sapiens

<400>  19

Tyr Gly Arg Lys Lys Arg Arg Gln Arg Arg Arg Gly Arg Phe Phe Lys 
1               5                   10                  15      


Ser Phe Gly 
            


