                         SEQUENCE LISTING

<110>  Trustees of Dartmouth College
       Madden, Dean R.
       Cushing, Patrick R.
       Boisguerin, Prisca
       Volkmer, Rudolf
       Vouilleme, Lars
 
<120>  THERAPY AND KIT FOR THE PREVENTION AND TREATMENT OF CYSTIC 
       FIBROSIS

<130>  DC0405WO.4

<150>  14/719,910
<151>  2015-05-22

<160>  49    

<170>  PatentIn version 3.5

<210>  1
<211>  6
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (1)..(1)
<223>  Xaa denotes Met, Phe, Leu, Ala or Trp

<220>
<221>  MISC_FEATURE
<222>  (2)..(2)
<223>  Xaa denotes Gln, Pro, or Phe

<220>
<221>  MISC_FEATURE
<222>  (3)..(3)
<223>  Xaa independently denotes Ser, Val or Thr

<220>
<221>  MISC_FEATURE
<222>  (4)..(4)
<223>  Xaa independently denotes Ser or Thr

<220>
<221>  MISC_FEATURE
<222>  (5)..(5)
<223>  Xaa denotes Lys or Ile

<220>
<221>  MISC_FEATURE
<222>  (6)..(6)
<223>  Xaa denotes  Ile or Val.

<400>  1

Xaa Xaa Xaa Xaa Xaa Xaa 
1               5       


<210>  2
<211>  11
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  2

Cys Ala Asn Gly Leu Met Gln Thr Ser Lys Ile 
1               5                   10      


<210>  3
<211>  9
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  3

Cys Gly Leu Met Gln Thr Ser Lys Ile 
1               5                   


<210>  4
<211>  7
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  4

Cys Phe Phe Ser Thr Ile Ile 
1               5           


<210>  5
<211>  7
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  5

Cys Phe Phe Thr Ser Ile Ile 
1               5           


<210>  6
<211>  7
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  6

Cys Met Gln Thr Ser Ile Ile 
1               5           


<210>  7
<211>  7
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  7

Cys Met Gln Thr Ser Lys Ile 
1               5           


<210>  8
<211>  7
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  8

Cys Trp Gln Thr Ser Ile Ile 
1               5           


<210>  9
<211>  7
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  9

Cys Trp Pro Thr Ser Ile Ile 
1               5           


<210>  10
<211>  8
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  10

Cys Thr Trp Gln Thr Ser Ile Ile 
1               5               


<210>  11
<211>  8
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  11

Cys Lys Trp Gln Thr Ser Ile Ile 
1               5               


<210>  12
<211>  8
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  12

Pro His Trp Gln Thr Ser Ile Ile 
1               5               


<210>  13
<211>  8
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  13

Phe His Trp Gln Thr Ser Ile Ile 
1               5               


<210>  14
<211>  8
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  14

Ser Arg Trp Gln Thr Ser Ile Ile 
1               5               


<210>  15
<211>  11
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  15

Cys Ala Asn Ser Arg Trp Gln Thr Ser Ile Ile 
1               5                   10      


<210>  16
<211>  8
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  16

Gly Leu Trp Pro Thr Ser Ile Ile 
1               5               


<210>  17
<211>  8
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  17

Ser Arg Trp Pro Thr Ser Ile Ile 
1               5               


<210>  18
<211>  8
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  18

Phe Pro Trp Pro Thr Ser Ile Ile 
1               5               


<210>  19
<211>  10
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (1)..(1)
<223>  Modified with fluorescein

<400>  19

Ala Asn Ser Arg Trp Pro Thr Ser Ile Ile 
1               5                   10  


<210>  20
<211>  10
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide

<400>  20

Ala Asn Ser Arg Trp Pro Thr Ser Ile Ile 
1               5                   10  


<210>  21
<211>  10
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  21

Ala Asn Ser Arg Leu Pro Thr Ser Ile Ile 
1               5                   10  


<210>  22
<211>  10
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  22

Ala Asn Ser Arg Ala Pro Thr Ser Ile Ile 
1               5                   10  


<210>  23
<211>  6
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  23

Trp Gln Val Thr Arg Val 
1               5       


<210>  24
<211>  6
<212>  PRT
<213>  Artificial Sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (1)..(1)
<223>  Xaa denotes Met, Phe, Leu, or Ala.

<220>
<221>  MISC_FEATURE
<222>  (2)..(2)
<223>  Xaa denotes Gln, Pro, or Phe.

<220>
<221>  MISC_FEATURE
<222>  (3)..(3)
<223>  Xaa denotes Ser, Val or Thr.

<220>
<221>  MISC_FEATURE
<222>  (4)..(4)
<223>  Xaa denotes Ser or Thr.

<220>
<221>  MISC_FEATURE
<222>  (5)..(5)
<223>  Xaa denotes Lys, Arg or Ile.

<220>
<221>  MISC_FEATURE
<222>  (6)..(6)
<223>  Xaa denotes Ile or Val.

<400>  24

Xaa Xaa Xaa Xaa Xaa Xaa 
1               5       


<210>  25
<211>  15
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (2)..(2)
<223>  D-amino acid residue.

<220>
<221>  MISC_FEATURE
<222>  (5)..(5)
<223>  Modified with fluorescein.

<400>  25

Trp Arg Phe Lys Lys Ala Asn Ser Arg Trp Pro Thr Ser Ile Ile 
1               5                   10                  15  


<210>  26
<211>  15
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (2)..(2)
<223>  D-amino acid residue.

<400>  26

Trp Arg Phe Lys Lys Ala Asn Ser Arg Trp Pro Thr Ser Ile Ile 
1               5                   10                  15  


<210>  27
<211>  15
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (2)..(2)
<223>  D-amino acid residue.

<220>
<221>  MISC_FEATURE
<222>  (5)..(5)
<223>  Modified with 6-carboxy-X-rhodamine.

<400>  27

Trp Arg Phe Lys Lys Ala Asn Ser Arg Trp Pro Thr Ser Ile Ile 
1               5                   10                  15  


<210>  28
<211>  10
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide.


<220>
<221>  MISC_FEATURE
<222>  (1)..(4)
<223>  D-amino acid residue.

<400>  28

Pro Asn Glu Ala Trp Pro Thr Ser Ile Ile 
1               5                   10  


<210>  29
<211>  10
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide.


<220>
<221>  MISC_FEATURE
<222>  (1)..(1)
<223>  D-amino acid residue.

<220>
<221>  MISC_FEATURE
<222>  (3)..(3)
<223>  D-amino acid residue.

<400>  29

Phe Asn Ala Arg Trp Gln Thr Ser Ile Ile 
1               5                   10  


<210>  30
<211>  10
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (1)..(1)
<223>  D-amino acid residue.

<400>  30

Phe Asn Ser Arg Trp Gln Thr Ser Ile Ile 
1               5                   10  


<210>  31
<211>  10
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (1)..(2)
<223>  D-amino acid residue.

<400>  31

Lys Asn Ser Arg Trp Gln Thr Ser Ile Ile 
1               5                   10  


<210>  32
<211>  10
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (1)..(2)
<223>  D-amino acid residue.

<400>  32

Pro Asn Ser Arg Trp Gln Thr Ser Ile Ile 
1               5                   10  


<210>  33
<211>  10
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (2)..(2)
<223>  D-amino acid residue.

<400>  33

Ala Asn Ser Arg Trp Gln Thr Ser Ile Ile 
1               5                   10  


<210>  34
<211>  5
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (2)..(2)
<223>  D-amino acid residue.

<400>  34

Trp Arg Phe Lys Lys 
1               5   


<210>  35
<211>  7
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  35

Leu Glu Val Leu Phe Gln Gly 
1               5           


<210>  36
<211>  6
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  36

Trp Gln Thr Ser Ile Ile 
1               5       


<210>  37
<211>  4
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  37

Thr Ser Ile Ile 
1               


<210>  38
<211>  10
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  38

Ala Asn Gly Leu Met Gln Thr Ser Lys Leu 
1               5                   10  


<210>  39
<211>  4
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide


<220>
<221>  MISC_FEATURE
<222>  (1)..(1)
<223>  Xaa denotes any amino acid residue.

<220>
<221>  MISC_FEATURE
<222>  (2)..(2)
<223>  Xaa denotes Ser or Thr.

<220>
<221>  MISC_FEATURE
<222>  (3)..(3)
<223>  Xaa denotes any amino acid residue.

<220>
<221>  MISC_FEATURE
<222>  (4)..(4)
<223>  Xaa denotes Leu, Val or Ile.

<400>  39

Xaa Xaa Xaa Xaa 
1               


<210>  40
<211>  10
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetice peptide

<400>  40

Thr Glu Glu Glu Val Gln Asp Thr Arg Leu 
1               5                   10  


<210>  41
<211>  6
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  41

Trp Gln Asp Ser Gly Ile 
1               5       


<210>  42
<211>  27
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  42

Gly Ala Leu Phe Leu Gly Phe Leu Gly Ala Ala Gly Ser Thr Met Gly 
1               5                   10                  15      


Ala Trp Ser Gln Pro Lys Lys Lys Arg Lys Val 
            20                  25          


<210>  43
<211>  8
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  43

Arg Arg Arg Arg Arg Arg Arg Arg 
1               5               


<210>  44
<211>  14
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  44

Gly Arg Lys Lys Arg Arg Gln Arg Arg Arg Pro Pro Gln Gln 
1               5                   10                  


<210>  45
<211>  27
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  45

Gly Trp Thr Leu Asn Ser Ala Gly Tyr Leu Leu Gly Lys Ile Asn Leu 
1               5                   10                  15      


Lys Ala Leu Ala Ala Leu Ala Lys Lys Ile Leu 
            20                  25          


<210>  46
<211>  21
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  46

Ala Gly Tyr Leu Leu Gly Lys Ile Asn Leu Lys Ala Leu Ala Ala Leu 
1               5                   10                  15      


Ala Lys Lys Ile Leu 
            20      


<210>  47
<211>  18
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  47

Lys Leu Ala Leu Lys Leu Ala Leu Lys Ala Leu Lys Ala Ala Leu Lys 
1               5                   10                  15      


Leu Ala 
        


<210>  48
<211>  27
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  48

Gly Ala Leu Phe Leu Ala Phe Leu Ala Ala Ala Leu Ser Leu Met Gly 
1               5                   10                  15      


Leu Trp Ser Gln Pro Lys Lys Lys Arg Lys Val 
            20                  25          


<210>  49
<211>  16
<212>  PRT
<213>  Artificial sequence

<220>
<223>  Synthetic peptide

<400>  49

Arg Gln Ile Lys Ile Trp Phe Gln Asn Arg Arg Met Lys Trp Lys Lys 
1               5                   10                  15      


