                         SEQUENCE LISTING

<110>  Saint Louis University
       Saint Louis University
 
<120>  PRENATAL ENZYME REPLACEMENT THERAPY

<130>  60216.2

<160>  2     

<170>  PatentIn version 3.3

<210>  1
<211>  1587
<212>  DNA
<213>  Artificial

<220>
<223>  synthetic sequence

<400>  1
ccacgtcgat tgcatctctg ggctccaggg ataaagcagg tcttggggtg caccatgatt     60

tcaccattct tagtactggc cattggcacc tgccttacta actccttagt gccagagaaa    120

gagaaagacc ccaagtactg gcgagaccaa gcgcaagaga cactgaaata tgccctggag    180

cttcagaagc tcaacaccaa cgtggctaag aatgtcatca tgttcctggg agatgggatg    240

ggtgtctcca cagtgacggc tgcccgcatc ctcaagggtc agctccacca caaccctggg    300

gaggagacca ggctggagat ggacaagttc cccttcgtgg ccctctccaa gacgtacaac    360

accaatgccc aggtccctga cagcgccggc accgccaccg cctacctgtg tggggtgaag    420

gccaatgagg gcaccgtggg ggtaagcgca gccactgagc gttcccggtg caacaccacc    480

caggggaacg aggtcacctc catcctgcgc tgggccaagg acgctgggaa atctgtgggc    540

attgtgacca ccacgagagt gaaccatgcc acccccagcg ccgcctacgc ccactcggct    600

gaccgggact ggtactcaga caacgagatg ccccctgagg ccttgagcca gggctgtaag    660

gacatcgcct accagctcat gcataacatc agggacattg acgtgatcat ggggggtggc    720

cggaaataca tgtaccccaa gaataaaact gatgtggagt atgagagtga cgagaaagcc    780

aggggcacga ggctggacgg cctggacctc gttgacacct ggaagagctt caaaccgaga    840

tacaagcact cccacttcat ctggaaccgc acggaactcc tgacccttga cccccacaat    900

gtggactacc tattgggtct cttcgagcca ggggacatgc agtacgagct gaacaggaac    960

aacgtgacgg acccgtcact ctccgagatg gtggtggtgg ccatccagat cctgcggaag   1020

aaccccaaag gcttcttctt gctggtggaa ggaggcagaa ttgaccacgg gcaccatgaa   1080

ggaaaagcca agcaggccct gcatgaggcg gtggagatgg accgggccat cgggcaggca   1140

ggcagcttga cctcctcgga agacactctg accgtggtca ctgcggacca ttcccacgtc   1200

ttcacatttg gtggatacac cccccgtggc aactctatct ttggtctggc ccccatgctg   1260

agtgacacag acaagaagcc cttcactgcc atcctgtatg gcaatgggcc tggctacaag   1320

gtggtgggcg gtgaacgaga gaatgtctcc atggtggact atgctcacaa caactaccag   1380

gcgcagtctc ctgtgcccct gcgccacgag acccacggcg gggaggacgt ggccgtcttc   1440

tccaagggcc ccatggcgca cctgctgcac ggcgtccacg agcagaacta cgtcccccac   1500

gtgatggcgt atgcagcctg catcggggcc aacctcggcc actgtgctcc tgccagctcg   1560

gcaggcagca ccggtgaagc agaagcc                                       1587


<210>  2
<211>  529
<212>  PRT
<213>  Artificial

<220>
<223>  synthetic sequence

<400>  2

Pro Arg Arg Leu His Leu Trp Ala Pro Gly Ile Lys Gln Val Leu Gly 
1               5                   10                  15      


Cys Thr Met Ile Ser Pro Phe Leu Val Leu Ala Ile Gly Thr Cys Leu 
            20                  25                  30          


Thr Asn Ser Leu Val Pro Glu Lys Glu Lys Asp Pro Lys Tyr Trp Arg 
        35                  40                  45              


Asp Gln Ala Gln Glu Thr Leu Lys Tyr Ala Leu Glu Leu Gln Lys Leu 
    50                  55                  60                  


Asn Thr Asn Val Ala Lys Asn Val Ile Met Phe Leu Gly Asp Gly Met 
65                  70                  75                  80  


Gly Val Ser Thr Val Thr Ala Ala Arg Ile Leu Lys Gly Gln Leu His 
                85                  90                  95      


His Asn Pro Gly Glu Glu Thr Arg Leu Glu Met Asp Lys Phe Pro Phe 
            100                 105                 110         


Val Ala Leu Ser Lys Thr Tyr Asn Thr Asn Ala Gln Val Pro Asp Ser 
        115                 120                 125             


Ala Gly Thr Ala Thr Ala Tyr Leu Cys Gly Val Lys Ala Asn Glu Gly 
    130                 135                 140                 


Thr Val Gly Val Ser Ala Ala Thr Glu Arg Ser Arg Cys Asn Thr Thr 
145                 150                 155                 160 


Gln Gly Asn Glu Val Thr Ser Ile Leu Arg Trp Ala Lys Asp Ala Gly 
                165                 170                 175     


Lys Ser Val Gly Ile Val Thr Thr Thr Arg Val Asn His Ala Thr Pro 
            180                 185                 190         


Ser Ala Ala Tyr Ala His Ser Ala Asp Arg Asp Trp Tyr Ser Asp Asn 
        195                 200                 205             


Glu Met Pro Pro Glu Ala Leu Ser Gln Gly Cys Lys Asp Ile Ala Tyr 
    210                 215                 220                 


Gln Leu Met His Asn Ile Arg Asp Ile Asp Val Ile Met Gly Gly Gly 
225                 230                 235                 240 


Arg Lys Tyr Met Tyr Pro Lys Asn Lys Thr Asp Val Glu Tyr Glu Ser 
                245                 250                 255     


Asp Glu Lys Ala Arg Gly Thr Arg Leu Asp Gly Leu Asp Leu Val Asp 
            260                 265                 270         


Thr Trp Lys Ser Phe Lys Pro Arg Tyr Lys His Ser His Phe Ile Trp 
        275                 280                 285             


Asn Arg Thr Glu Leu Leu Thr Leu Asp Pro His Asn Val Asp Tyr Leu 
    290                 295                 300                 


Leu Gly Leu Phe Glu Pro Gly Asp Met Gln Tyr Glu Leu Asn Arg Asn 
305                 310                 315                 320 


Asn Val Thr Asp Pro Ser Leu Ser Glu Met Val Val Val Ala Ile Gln 
                325                 330                 335     


Ile Leu Arg Lys Asn Pro Lys Gly Phe Phe Leu Leu Val Glu Gly Gly 
            340                 345                 350         


Arg Ile Asp His Gly His His Glu Gly Lys Ala Lys Gln Ala Leu His 
        355                 360                 365             


Glu Ala Val Glu Met Asp Arg Ala Ile Gly Gln Ala Gly Ser Leu Thr 
    370                 375                 380                 


Ser Ser Glu Asp Thr Leu Thr Val Val Thr Ala Asp His Ser His Val 
385                 390                 395                 400 


Phe Thr Phe Gly Gly Tyr Thr Pro Arg Gly Asn Ser Ile Phe Gly Leu 
                405                 410                 415     


Ala Pro Met Leu Ser Asp Thr Asp Lys Lys Pro Phe Thr Ala Ile Leu 
            420                 425                 430         


Tyr Gly Asn Gly Pro Gly Tyr Lys Val Val Gly Gly Glu Arg Glu Asn 
        435                 440                 445             


Val Ser Met Val Asp Tyr Ala His Asn Asn Tyr Gln Ala Gln Ser Pro 
    450                 455                 460                 


Val Pro Leu Arg His Glu Thr His Gly Gly Glu Asp Val Ala Val Phe 
465                 470                 475                 480 


Ser Lys Gly Pro Met Ala His Leu Leu His Gly Val His Glu Gln Asn 
                485                 490                 495     


Tyr Val Pro His Val Met Ala Tyr Ala Ala Cys Ile Gly Ala Asn Leu 
            500                 505                 510         


Gly His Cys Ala Pro Ala Ser Ser Ala Gly Ser Thr Gly Glu Ala Glu 
        515                 520                 525             


Ala 
    


