                         SEQUENCE LISTING

<110>  INSERM
 
<120>  METHODS AND PHARMACEUTICAL COMPOSITION FOR THE TREATMENT OF 
       HUNTINGTON'S DISEASE

<130>  BIO10491CABOCHE

<160>  6     

<170>  PatentIn version 3.3

<210>  1
<211>  2138
<212>  DNA
<213>  Homo sapiens

<400>  1
atgagccccg ggctgctgct gctcggcagc gccgtcctgc tcgccttcgg cctctgctgc     60

accttcgtgc accgcgctcg cagccgctac gagcacatcc ccgggccgcc gcggcccagt    120

ttccttctag gacacctccc ctgcttttgg aaaaaggatg aggttggtgg ccgtgtgctc    180

caagatgtgt ttttggattg ggctaagaag tatggacctg ttgtgcgggt caacgtcttc    240

cacaaaacct cagtcatcgt cacgagtcct gagtcggtta agaagttcct gatgtcaacc    300

aagtacaaca aggactccaa gatgtaccgt gcgctccaga ctgtgtttgg tgagagactc    360

ttcggccaag gcttggtgtc cgaatgcaac tatgagcgct ggcacaagca gcggagagtc    420

atagacctgg ccttcagccg gagctccttg gttagcttaa tggaaacatt caacgagaag    480

gctgagcagc tggtggagat tctagaagcc aaggcagatg ggcagacccc agtgtccatg    540

caggacatgc tgacctacac cgccatggac atcctggcca aggcagcttt tgggatggag    600

accagtatgc tgctgggtgc ccagaagcct ctgtcccagg cagtgaaact tatgttggag    660

ggaatcactg cgtcccgcaa cactctggca aagttcctgc cagggaagag gaagcagctc    720

cgggaggtcc gggagagcat tcgcttcctg cgccaggtgg gcagggactg ggtccagcgc    780

cgccgggaag ccctgaagag gggcgaggag gttcctgccg acatcctcac acagattctg    840

aaagctgaag agggagccca ggacgacgag ggtctgctgg acaacttcgt caccttcttc    900

attgctggtc acgagacctc tgccaaccac ttggcgttca cagtgatgga gctgtctcgc    960

cagccagaga tcgtggcaag gctgcaggcc gaggtggatg aggtcattgg ttctaagagg   1020

tacctggatt tcgaggacct ggggagactg cagtacctgt cccaggtcct caaagagtcg   1080

ctgaggctgt acccaccagc atggggcacc tttcgcctgc tggaagagga gaccttgatt   1140

gatggggtca gagtccccgg caacaccccg ctcttgttca gcacctatgt catggggcgg   1200

atggacacat actttgagga cccgctgact ttcaaccccg atcgcttcgg ccctggagca   1260

cccaagccac ggttcaccta cttccccttc tccctgggcc accgctcctg catcgggcag   1320

cagtttgctc agatggaggt gaaggtggtc atggcaaagc tgctgcagag gctggagttc   1380

cggctggtgc ccgggcagcg cttcgggctg caggagcagg ccacactcaa gccactggac   1440

cccgtgctgt gcaccctgcg gccccgcggc tggcagcccg cacccccacc acccccctgc   1500

tgagggggcc tccaggcagg acgagactcc tcgggcaagg gccgtgcccg cccacctctg   1560

ctgcccacgg ccacccaccc ttctcccctg ccccgtcccc tgggccaccc ttcacgctgg   1620

cttccagcgg gccctctgcc gaccgcctgc ttcacacccc tcagcgctcc ctgtcgcctg   1680

cggactccat ggcccttcct ggactggccc ttgcccaact cccagccacc accactgtcc   1740

ctaccactga gcccttgcac aggccacttg ctcagacgag acaccctaac tcttgctcac   1800

tccctaaagc cctcttcagg ggtcacctcc tccaagaagc cctccttgcc accccccgcc   1860

ggcaggggcc cctcctctgt gctccctcgg tcacctgtgc tacctctaac accacactga   1920

ccacactgta tcgtgagtgt ccgttgacgt gaccaattgc cctgccaggc tgtcagcgcc   1980

tcaagggtag ggtctgcgtg tgatttgtct ctgagccccc tgtgcccacc cagggcccgg   2040

cacagagtcg atgctcaata aatgtgtgtt gactgcaaaa aaaaaaaaaa aaaaaaaaaa   2100

aaaaaaaaaa aaaaaaaaaa aaaaaaaaaa aaaaaaaa                           2138


<210>  2
<211>  500
<212>  PRT
<213>  Homo sapiens

<400>  2

Met Ser Pro Gly Leu Leu Leu Leu Gly Ser Ala Val Leu Leu Ala Phe 
1               5                   10                  15      


Gly Leu Cys Cys Thr Phe Val His Arg Ala Arg Ser Arg Tyr Glu His 
            20                  25                  30          


Ile Pro Gly Pro Pro Arg Pro Ser Phe Leu Leu Gly His Leu Pro Cys 
        35                  40                  45              


Phe Trp Lys Lys Asp Glu Val Gly Gly Arg Val Leu Gln Asp Val Phe 
    50                  55                  60                  


Leu Asp Trp Ala Lys Lys Tyr Gly Pro Val Val Arg Val Asn Val Phe 
65                  70                  75                  80  


His Lys Thr Ser Val Ile Val Thr Ser Pro Glu Ser Val Lys Lys Phe 
                85                  90                  95      


Leu Met Ser Thr Lys Tyr Asn Lys Asp Ser Lys Met Tyr Arg Ala Leu 
            100                 105                 110         


Gln Thr Val Phe Gly Glu Arg Leu Phe Gly Gln Gly Leu Val Ser Glu 
        115                 120                 125             


Cys Asn Tyr Glu Arg Trp His Lys Gln Arg Arg Val Ile Asp Leu Ala 
    130                 135                 140                 


Phe Ser Arg Ser Ser Leu Val Ser Leu Met Glu Thr Phe Asn Glu Lys 
145                 150                 155                 160 


Ala Glu Gln Leu Val Glu Ile Leu Glu Ala Lys Ala Asp Gly Gln Thr 
                165                 170                 175     


Pro Val Ser Met Gln Asp Met Leu Thr Tyr Thr Ala Met Asp Ile Leu 
            180                 185                 190         


Ala Lys Ala Ala Phe Gly Met Glu Thr Ser Met Leu Leu Gly Ala Gln 
        195                 200                 205             


Lys Pro Leu Ser Gln Ala Val Lys Leu Met Leu Glu Gly Ile Thr Ala 
    210                 215                 220                 


Ser Arg Asn Thr Leu Ala Lys Phe Leu Pro Gly Lys Arg Lys Gln Leu 
225                 230                 235                 240 


Arg Glu Val Arg Glu Ser Ile Arg Phe Leu Arg Gln Val Gly Arg Asp 
                245                 250                 255     


Trp Val Gln Arg Arg Arg Glu Ala Leu Lys Arg Gly Glu Glu Val Pro 
            260                 265                 270         


Ala Asp Ile Leu Thr Gln Ile Leu Lys Ala Glu Glu Gly Ala Gln Asp 
        275                 280                 285             


Asp Glu Gly Leu Leu Asp Asn Phe Val Thr Phe Phe Ile Ala Gly His 
    290                 295                 300                 


Glu Thr Ser Ala Asn His Leu Ala Phe Thr Val Met Glu Leu Ser Arg 
305                 310                 315                 320 


Gln Pro Glu Ile Val Ala Arg Leu Gln Ala Glu Val Asp Glu Val Ile 
                325                 330                 335     


Gly Ser Lys Arg Tyr Leu Asp Phe Glu Asp Leu Gly Arg Leu Gln Tyr 
            340                 345                 350         


Leu Ser Gln Val Leu Lys Glu Ser Leu Arg Leu Tyr Pro Pro Ala Trp 
        355                 360                 365             


Gly Thr Phe Arg Leu Leu Glu Glu Glu Thr Leu Ile Asp Gly Val Arg 
    370                 375                 380                 


Val Pro Gly Asn Thr Pro Leu Leu Phe Ser Thr Tyr Val Met Gly Arg 
385                 390                 395                 400 


Met Asp Thr Tyr Phe Glu Asp Pro Leu Thr Phe Asn Pro Asp Arg Phe 
                405                 410                 415     


Gly Pro Gly Ala Pro Lys Pro Arg Phe Thr Tyr Phe Pro Phe Ser Leu 
            420                 425                 430         


Gly His Arg Ser Cys Ile Gly Gln Gln Phe Ala Gln Met Glu Val Lys 
        435                 440                 445             


Val Val Met Ala Lys Leu Leu Gln Arg Leu Glu Phe Arg Leu Val Pro 
    450                 455                 460                 


Gly Gln Arg Phe Gly Leu Gln Glu Gln Ala Thr Leu Lys Pro Leu Asp 
465                 470                 475                 480 


Pro Val Leu Cys Thr Leu Arg Pro Arg Gly Trp Gln Pro Ala Pro Pro 
                485                 490                 495     


Pro Pro Pro Cys 
            500 


<210>  3
<211>  20
<212>  DNA
<213>  Artificial

<220>
<223>  Primer

<400>  3
tcctctcctg ttcagcacct                                                 20


<210>  4
<211>  20
<212>  DNA
<213>  Artificial

<220>
<223>  Primer

<400>  4
ggccatgaca actttcacct                                                 20


<210>  5
<211>  22
<212>  DNA
<213>  Artificial

<220>
<223>  Primer

<400>  5
ttgctcgaga tgtcatgaag ga                                              22


<210>  6
<211>  24
<212>  DNA
<213>  Artificial

<220>
<223>  Primer

<400>  6
agcaggtcag caaagaactt atag                                            24


